Homme de 54ans. Alcoolo-‐tabagique, antécédent de pancréa te aiguë. Diagnos c. Cavernome porte. Lacis veineux péri-‐portal. Varices péri-‐spléniques. B. Condat, V. Vilgrain, T. Asselah, D. O’Toole, P. Rufat, M. Zappa, et cavernoma-associated cholangiopathy: a clinical and MR-cholangiography. The portal for rare diseases and orphan drugs. Orphanet, the mobile portal for rare diseases – MOBILE HEALTH · Sitemap · Legal notice · Cookies · Career.
|Published (Last):||11 January 2009|
|PDF File Size:||13.29 Mb|
|ePub File Size:||11.52 Mb|
|Price:||Free* [*Free Regsitration Required]|
Cavernous transformation of the portal vein CTPV is a sequela of portal vein thrombosis and is the replacement of the normal single channel portal vein with numerous tortuous venous channels. For a discussion of demographics and presentation, please refer to the article on portal vein thrombosis.
Following thrombosis, the portal vein may or may not re-canalize. Re-canalisation is seen more frequently in patients without cirrhosis or disease of the liver leading to inherently increased resistance to portal flow. In patients whose portal vein does not recanalize, or only partially re-canalizes, collateral veins thought to be paracholedochal veins dilate and become serpiginous.
These vessels drain variably into the left and right portal veins or more distally into the liver. Additional communications can cavernime be identified with the pericholecystic veins. CTPV is most of the times inefficient in guaranteeing adequate portal vein inflow to the liver parenchyma far from the hilum and, therefore, is associated with an increased hepatic arterial flow to those peripheral liver segments.
These changes lead to a central liver hypertrophy and peripheral liver atrophy 8. In addition to direct visualization of the dilated vessels, the resultant portal hypertension results in other frequent changes: Additionally, there are changes in liver shape which are somewhat different to those seen in cirrhosis 2.
Typically these changes are:. Cvaernome examination can be carried out at the same time to evaluate for portal hypertension.
Cavernous transformation appears as numerous tortuous vessels occupying the portal vein bed. Flow is generally hepatopetal and continuous with little if any respiratory or cardiac variation 4.
MRI is also a proven method for imaging the portal venous system and may be used as a complementary or alternative modality to CT. MRI is usually reserved to clarify associated benign hepatocellular nodules that may be seen in up to a fifth of the patients, particularly the focal nodular hyperplasia -like lesions 8.
Whereas portal hypertension can in some cases be treated caverhome TIPSthe absence of normal portal circulation usually makes this impossible. You can also scroll through stacks with your mouse wheel or the keyboard arrow keys. Unable to process the form. Check for errors and try again. Thank you for updating your details. Log in Sign up.
Articles Cases Courses Quiz. About Blog Go ad-free. Pathology Radiographic features Treatment and prognosis References Images: Cavernous transformation of the portal vein: Edit article Share article View revision history. Synonyms or Alternate Spellings: Support Radiopaedia and see fewer ads.
Orphanet: Cavernome cerebral
Case 1 Case 1. Case 2 Case 2. Case 3 Case 3. Case 4 Case 4. Case 5 Case 5. Case 9 Case 9. Case 10 Case Loading Stack – 0 images remaining.